Abstract
We report the case of a 14 y.o girl treated with radiotherapy for an
abdominal paraganglioma - rare pediatric abdominal tumor - with
macroscopic tumoral residue after initial surgery and bone metastasis at
diagnosis. Irradiation of the tumoral residue and adjacent vertebral
metastasis was decided in national committee, proton or photon
based-irradiations were compared, before choosing helical tomotherapy
photonic irradiation to better protect kidneys. Response at three months
was mixed, with mild regression on the tumoral residue contrasting with
bone progression. The patient is now under screening to enter a
prospective phase II trial of peptide receptor radionuclide therapy
(PPRT).