A CASE SERIES OF RARE AND AGGRESSIVE EXTRA CRANIAL MALIGNANT RHABDOID
TUMORS.
Abstract
Malignant rhabdoid tumors (MRT) are very aggressive neoplasms seen in
infantile age groups. A high index of suspicion is needed for early
diagnosis. They are small round cell tumors with characteristic loss of
INI -1 expression. Here we present a case series of 6 rhabdoid tumors
diagnosed over 2 years, of which 4 of them presented as soft tissue
swelling neck and chest wall. All of them had a very short duration of
presentation and despite timely diagnosis, 4 of them progressed while on
treatment and resulted in mortality.