Case Source of pulmonary blood flow Source of pulmonary blood flow Origin of MAPCAs Origin of MAPCAs MPA MPA Confluence of PA Confluence of PA RPA/LPA RPA/LPA Postnatal outcome
Fetal PN Fetal PN Fetal PN Fetal PN Fetal PN
1. Double MAPCA Descending aorta Descending aorta + aortic arch - - +* - +*/+* -/- Complete cardiac repair, alive
2. Double Double Descending aorta Descending aorta + + + + +/+ +/+ Complete cardiac repair, alive
3. MAPCA MAPCA Descending aorta Descending aorta + + + + +/+ +/+ Complete cardiac repair, alive
4. Double Double Coronary artery Coronary artery - - - - +/+ +/+ Stepped surgery, scheduled for total repair, alive
5. DA DA 0 0 + + + + +/+ +/+ Mortality without surgery (Tr13)
6. DA DA 0 0 + + + + +/+ +/+ Complete cardiac repair, alive
7. MAPCAs MAPCA Descending aorta Descending aorta - - - - -/- -/- Mortality without surgery (Tr18, MCDK)
8. Double MAPCA Descending aorta Descending aorta + aortic arch + - + + +/+ +/+ Postoperative mortality
9. MAPCAs MAPCA Descending aorta Descending aorta - + - - -/- +*/+* Complete cardiac repair, alive
10. MAPCAs MAPCA Descending aorta Descending aorta - - - - -/- +*/+* Postoperative mortality
11. DA DA 0 0 +* + + + +*/+* +*/+* Postoperative mortality (Di George)
12. MAPCA MAPCA Descending aorta Descending aorta - - - - -/- -/- Mortality without surgery
13. DA DA 0 0 + + + + +/+ +/+ Mortality without surgery (Giant omphalocele)
14. DA DA 0 0 + + + + +/+ +/+ Complete cardiac repair, alive
15. DA DA 0 0 + + + + +/+ +/+ Postoperative mortality after the first stage (DWM)
16. DA DA 0 0 +* + + + +*/+* +*/+* Complete cardiac repair, alive
17. DA DA 0 0 + + + + +/+ +/+ Stepped surgery, scheduled for total repair, alive
PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure PN: postnatal, DA: ductus arteriosus, RPA: right pulmonary artery, LPA: left pulmonary artery, MCDK: multicystic dysplastic kidneys, DWM: Dandy-Walker malformation, * severely hypoplastic/ not possible to measure