Cardiorrhexis due to primary angiosarcoma of the heart
- Sowjanya Yenigalla,
- Hanneke Dannheimer,
- Farouk Mookadam,
- Anupa Patel
Sowjanya Yenigalla
Banner - University Medical Center Phoenix
Author ProfileFarouk Mookadam
Banner - University Medical Center Phoenix
Author ProfileAbstract
38 year old young female presented with a two-week history of dyspnoea
and general malaise without any other clinical signs of malignancy.
Two-dimensional Echocardiogram showed findings suspicious for a right
atrial mass. Transoesophageal echocardiogram showed rupture of the right
atrial free wall with a pseudoaneurysm and mass that has also
infiltrated the right ventricle. Histopathology of the biopsied
specimens confirmed the diagnosis of cardiac angiosarcoma. Given its
rapid growth, nonspecific symptoms and late presentation to the
hospital, diagnosis is often delayed. Early diagnosis is key as these
patients can be referred to surgery sooner than later due to rapid
progression of the mass and poor survival rates. Unfortunately, our
patient had brain and lung metastases and local tissue destruction by
the time she presented to the hospital. Echocardiography plays a crucial
role as a readily available imaging technique to help locate the tumour
and define its extent.