Yacoub valve-sparing aortic root replacement with a concomitant repair of Tetralogy of Fallot: a case reportJuan Wu1, MB, Qi An2, MD, Yongjun Qian2, MD, PhD1Out-patient Department, West China Hospital, Sichuan University, 37 Guoxue Lane, Chengdu, Sichuan 610041, China2Department of Cardiovascular Surgery, West China Hospital, Sichuan University, 37 Guoxue Lane, Chengdu, Sichuan 610041, ChinaCorresponding Author: Dr. Yongjun Qian, MD, PhDE-mail: [email protected]

Here we report a case of a previously unoperated 35-year-old male TOF patient. He was admitted due to dyspnea, initial physical examination demonstrated cyanosis and heart murmurs. Echocardiography suggested secundum atrial septal defect, perimembranous ventricular septal defect and mild-severe aortic regurgitation. Computed tomography angiography indicated aortic root dilation and suspicious right coronary artery aneurysm. Concurrent repair of TOF and VSARR was performed successfully and the patient had a satisfactory recovery.

A case of Berry syndrome: a rare congenital cardiac structural abnormality with one-stage surgical repair Shanshan Ma1, Bi Wen1, Qi An2, Xin Zhang1*1Department of Cardiology, West China Hospital, Sichuan University, Guoxuexiang 37th, 610041 Chengdu, Sichuan, P.R. China2Department of Cardiovascular Surgery, West China Hospital, Sichuan University, 37 Guoxue Lane, Chengdu, Sichuan 610041, China*Corresponding Author: Dr. Xin Zhang, MBE-mail: [email protected]

In this case, we reported a 24-day-old infant with a rare combination of the anomalous origin of coronary artery and the type A interrupted aortic arch, who presented with significant shortness of breath. Besides these anomalies, further cardiac examination including transthoracic echocardiography and CT angiogram revealed ventricular septum defect, patent foramen ovale and patent ductus arteriosus at the same time. Surgical procedures including repair of ventricular septum defect, ligation of patent ductus arteriosus, unroofing of right coronary artery and end-to-side aortic anastomosis were performed to cure the infant. This patient stayed in ICU for few days without any major complications and discharged from hospital at the tenth day after surgery.

In this case report, we describe a rare large right ventricular fibroma with sudden chest pain in a 9 year old child. The tumor was successfully surgical removed under cardiopulmonary bypass, but there was only a small remnant of the tumor to avoid rupture of the right ventricle and injury to the tricuspid valve. Pathological examination confirmed that the tumor was fibrous borderline tumor. The patient's heart function and the size of atrium and ventricles were normal, and there was no tricuspid regurgitation at 3-months follow-up. It was reported that the age less than 17 years old at time of diagnosis are associated with a poor prognosis, the long term outcome for this children patient needs further follow-up.

Aortopulmonary window (APW) is a rare but serious congenital cardiac malformation, most patients with APW will die from congestive heart failure a few months after birth. However, in this case we presented is an extremely rare condition that consist of a type III APW and a ductus arteriosus originated left pulmonary artery. Preoperative diagnosis included echocardiography and chest computerized tomography revealed anatomical structure of the heart and great vessel clearly, cardiac catheterization indicated that the pulmonary resistances indices were 2.92 wood U⁄m^2 in LPA and 3.35 wood U⁄m^2 in RPA, Qp:Qs was 3.26. This patient underwent surgical correction at the age of 9 and successfully survived.