Abstract

Cardiac rhabdomyoma is the most common primary heart tumor in childhood. This tumor, which is frequently associated with tuberous sclerosis complex, mostly disappears in childhood with spontaneous regression. Surgical resection is required in case of outflow obstruction, arrhythmia and protruding enough to disrupt the filling of the heart cavities. There are very few case series in the literature about rhabdomyom, whose relationship with other congenital heart defects has not been clearly demonstrated. In this case of tuberous sclerosis we presented to you, we reported our approach to the tumor during the corrective surgery of the infant, who was diagnosed with atrioventricular septal defect and patent ductus arteriosus, and rhabdomyoma accompanying these malformations.